A Study to Determine the Long-Term Safety, Tolerability and Biological Activity of SAR421869 in Patients With Usher Syndrome Type 1B

2024-513500-34-00 Protocol LTS13619 Therapeutic exploratory (Phase II) Ongoing, recruitment ended

Start 9 Nov 2015 · Status Ongoing, recruitment ended · 1 EU/EEA countries · 1 sites · Protocol LTS13619

Overview

Sponsor-declared trial summary

Phase Therapeutic exploratory (Phase II)
Status Ongoing, recruitment ended
Participants planned 9
Countries 1
Sites 1

Usher's syndrome

To evaluate the long-term safety and tolerability of SAR421869 in patients with Usher syndrome Type 1B

Key facts

Sponsor
Sanofi-Aventis Recherche & Developpement
Participant type
Patients
Age range
18-64 years
Gender
Male and Female
Therapeutic area
Diseases [C] - Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16]
Trial duration
9 Nov 2015 → ongoing
Decision date (initial)
2024-09-12
Transition trial
Yes
Low-intervention
No
Rare-disease indication
Yes
Vulnerable population
Yes
Funding sources
Sanofi-Aventis Recherche & Développement

External identifiers

EU CT number
2024-513500-34-00
EudraCT number
2013-000597-29

Trial design

CTIS Part I — objectives, methods, condition coding

Main objective

Scope: Efficacy, Safety

To evaluate the long-term safety and tolerability of SAR421869 in patients with Usher syndrome Type 1B

Secondary objectives 1

  1. To assess long-term safety and biological activity of SAR421869

Conditions and MedDRA coding

Usher's syndrome

VersionLevelCodeTermSystem organ class
20.0 PT 10063396 Usher's syndrome 100000004850

Eligibility criteria

Principal inclusion / exclusion criteria as submitted by sponsor

Inclusion criteria 3

  1. Provide signed and dated written informed consent (and if appropriate assent) and any locally required authorization eg, Health Insurance Portability and Accountability Act (HIPAA).
  2. Must have been enrolled in protocol TDU13600.
  3. Must have received a subretinal injection of SAR421869

Exclusion criteria 1

  1. Did not receive SAR421869 as part of the TDU13600 protocol.

Endpoints

Primary and secondary outcome measures (English text)

Primary endpoints 1

  1. The incidence of adverse events

Secondary endpoints 2

  1. Clinically important changes in ocular safety assessments
  2. Delay in retinal degeneration

Investigational products

Investigational medicinal products (IMPs), comparators, placebo, auxiliary

Test 1

SAR421869

PRD11418033 · Product

Active substance
Lentiviral Vector Derived From the Equine Infectious Anaemia Virus Containing the Human MYO7A Gene
Substance synonyms
Lentiviral vector derived from the equine infectious anaemia virus containing the human myosin VIIA gene, Lentiviral vector containing the human MYO7A gene, SAR421869, UshStat
Pharmaceutical form
SUSPENSION FOR INJECTION
Route of administration
UNKNOWN USE
Max daily dose
0 DF dosage form
Max total dose
0 DF dosage form
Max treatment duration
1 Day(s)
Authorisation status
Not Authorised
MA holder
SANOFI AVENTIS RECHERCHE ET DEVELOPPEMENT (SAR)
Paediatric formulation
No
Orphan designation
Yes
Orphan designation number
EU / 3 / 10 / 727

Sponsors and contacts

Sponsor organisations, regulatory contacts, third parties

Sanofi-Aventis Recherche & Developpement

Sponsor organisation
Sanofi-Aventis Recherche & Developpement
Address
13 Quai Jules Guesde
City
Vitry Sur Seine
Postcode
94400
Country
France

Scientific contact point

Organisation
Sanofi-Aventis Recherche & Developpement
Contact name
Clinical Sciences and Operations

Public contact point

Organisation
Sanofi-Aventis Recherche & Developpement
Contact name
Clinical Sciences and Operations

Third parties 2

OrganisationCity, countryDuties
The Emmes Company LLC
ORG-100048299
Rockville, United States Data management
ESMS Global Limited
ORG-100023149
London, United Kingdom Other

Locations

1 EU/EEA country · 1 investigational sites

By country

CountryMS statusPlanned subjectsSites
France Ongoing, recruitment ended 4 1
Rest of world
United States
5

Investigational sites

France

1 site · Ongoing, recruitment ended
Quinze-Vingts National Ophthalmology Hospital
Ophtalomogy, 28 Rue De Charenton, 75012, Paris

Country notifications

Trial-start, recruitment-start, end and early-termination notifications submitted per Member State

Country Trial startTrial end Recruitment startRecruitment end Early termination
France 2015-11-09 2015-11-09 2018-03-08

Results and documents

Annex IV summary of results, Annex V layperson summary, and all documents registered in CTIS for this trial

Documents 5 files

Public protocol annexes, IB summaries, regulatory submissions and post-authorisation documents registered in CTIS.

TypeTitleVersion
Protocol (for publication) d1-rdct-protocol-en-2024-513500-34 2
Recruitment arrangements (for publication) K1-recruitment-arrangements-en-waiver 1
Subject information and informed consent form (for publication) L1-sis-icf-addendum-fr 1
Subject information and informed consent form (for publication) L1-sis-icf-main-fr 2
Synopsis of the protocol (for publication) d1-lay-protocol-synopsis-en-2024-513500-34 1

Application history

2 submissions — initial application plus substantial / non-substantial modifications

#TypeCodeSubmittedReference MSConclusionDecision date
1 INITIAL IN 2024-07-30 France Acceptable
2024-09-12
2024-09-12
2 NON SUBSTANTIAL MODIFICATION NSM-1 2026-04-01 France Acceptable
2024-09-12
2026-04-01