Prediction and prevention of infantile spasms in high risk children

2024-517488-22-00 Therapeutic use (Phase IV) Ongoing, recruiting

Start 28 May 2018 · Status Ongoing, recruiting · 1 EU/EEA countries · 15 sites

Overview

Sponsor-declared trial summary

Phase Therapeutic use (Phase IV)
Status Ongoing, recruiting
Participants planned 140
Countries 1
Sites 15

Patients in high risk for infantile spasm syndrome (age under 1 yr old): -tuborous sclerosis (not after 11/2023) -large vascular cortical injury (large infarction/hemorrhage/infection/trauma, HIE II-III including MRI-criteria 2b and 3, with also cortical lesions -grade IV intraventricular hemorrhage (including hemorrhagic infarct in brain parenchyma) -grade III-IV PVL (including porencephalic cyst) in preterms

This study aims to prevent infantile spasm syndrome in high risk children (tuberous sclerosis or large vascular injury) under 1-yr old by vigabatrin prophylactic medication.

Key facts

Sponsor
HUS-Yhtymae
Participant type
Pediatric, Patients
Age range
0-17 years
Gender
Male and Female
Therapeutic area
Diseases [C] - Nervous System Diseases [C10]
Trial duration
28 May 2018 → ongoing
Decision date (initial)
2024-09-13
Transition trial
Yes
Low-intervention
No
Rare-disease indication
Yes
Vulnerable population
Yes

External identifiers

EU CT number
2024-517488-22-00
EudraCT number
2017-004775-30

Trial design

CTIS Part I — objectives, methods, condition coding

Main objective

Scope: Prophylaxis

This study aims to prevent infantile spasm syndrome in high risk children (tuberous sclerosis or large vascular injury) under 1-yr old by vigabatrin prophylactic medication.

Conditions and MedDRA coding

Patients in high risk for infantile spasm syndrome (age under 1 yr old): -tuborous sclerosis (not after 11/2023) -large vascular cortical injury (large infarction/hemorrhage/infection/trauma, HIE II-III including MRI-criteria 2b and 3, with also cortical lesions -grade IV intraventricular hemorrhage (including hemorrhagic infarct in brain parenchyma) -grade III-IV PVL (including porencephalic cyst) in preterms

Eligibility criteria

Principal inclusion / exclusion criteria as submitted by sponsor

Inclusion criteria 1

  1. All children aged <1yr old with tuberous sclerosis (but not anymore after 11/2023), or large vascular cortical injury (large infarc-tion/hemorrhage/infection/trauma, HIE II-III including MRI criteria 2b and 3 involving cortical lesion or early stage MRI, imaged within first 5 days, general swelling of the cerebrum hemispheres and simultaneous extensive cortical/subcortical restricted diffusion finding in the ADC map). Large cortical injury is defined as almost the whole area of a. cerebri anterior or posterior, or about half of the area of a. cerebri media. Additionally, a grade IV intraventricular hemorrhage (including hemorrhagic infarction in the parenchyma) or grade III-IV PVL (containing porencephalic cyst) in premature infants. Brain MRI must have been done earlier as a part of normal clinical diagnostics.Parents must have sufficient Finnish, Swedish or English (or the native language of the research center country) language skills.

Exclusion criteria 1

  1. Patient has not allowed to have received VGB for any reason before. A patient will not be recruited if he/she is already participating in another medication intervention study, or the cause of the cortical injury is child abuse. Or child has had infantile spasms before.

Endpoints

Primary and secondary outcome measures (English text)

Primary endpoints 1

  1. Efficacy: whether patient gets infantile spasm syndrome or not

Secondary endpoints 1

  1. Is there a difference between groups in neurocognitive development? Can eye tracking analysis predict EEG changes, neurocognitive development or onset of infantile spasm syndrome?

Investigational products

Investigational medicinal products (IMPs), comparators, placebo, auxiliary

Test 1

Sabrilex 500 mg rakeet oraaliliuosta varten

PRD482281 · Product

Active substance
Vigabatrin
Pharmaceutical form
GRANULES FOR ORAL SOLUTION
Route of administration
ORAL
Max daily dose
150 mg/kg milligram(s)/kilogram
Max total dose
150 mg/kg milligram(s)/kilogram
Max treatment duration
11 Month(s)
Authorisation status
Authorised
ATC code
N03AG04 — VIGABATRIN
Marketing authorisation
11148
MA holder
SANOFI OY
MA country
Finland
Paediatric formulation
No
Orphan designation
No
Modified vs. Marketing Authorisation
No

Sponsors and contacts

Sponsor organisations, regulatory contacts, third parties

HUS-Yhtymae

Sponsor organisation
HUS-Yhtymae
Address
Stenbackinkatu 9
City
Helsinki
Postcode
00290
Country
Finland

Scientific contact point

Organisation
HUS-Yhtymae
Contact name
HUS Helsinki University Hospital, New Children’s Hospital, pediatric neurology

Public contact point

Organisation
HUS-Yhtymae
Contact name
HUS Helsinki University Hospital, New Children’s Hospital, pediatric neurology

Locations

1 EU/EEA country · 15 investigational sites

By country

CountryMS statusPlanned subjectsSites
Finland Ongoing, recruiting 140 15
Rest of world 0

Investigational sites

Finland

15 sites · Ongoing, recruiting
Kymenlaakso Central Hospital
Pediatric Neurology, Kotkantie 41, 48210, Kotka
HUS-Yhtymae (Helsinki University Hospital/The New Children's hospital)
Pediatric Neurology, PL 280, 00029, HUS
Central Hospital in Kemi (Länsi-Pohja Central Hospital)
Pediatric Neurology, Kauppakatu 25, 94100, Kemi
Lahti Central Hospital
Pediatric Neurology, Keskussairaalankatu 7, 15850, Lahti
Tampere University Hospital
Pediatric Neurology, Elamanaukio 2, 33520, Tampere
Turku University Hospital
Pediatric Neurology, Kiinamyllynkatu 4-8, 20520, Turku
South Karelia Central Hospital
Pediatric Neurology, Valto Kakelan Katu 1, 53130, Lappeenranta
HUS-Yhtymae
P, Sairaalankatu 1, 05850, Hyvinkaa
Central Finland Hospital District Central Finland Hospital Nova
Pediatric Neurology, Hoitajantie 3, 40620, Jyvaskyla
Seinäjoki Central Hospital
Pediatric Neurology, Hanneksenrinne 7, 60220, Seinäjoki
Kainuu Central Hospital
Pediatric Neurology, Sotkamontie 13, 87300, Kajaani
Oulu University Hospital
Pediatric Neurology, Kajaanintie 50, 90220, Oulu
Kanta-Hame Central Hospital
Pediatri, Ahvenistontie 20, 13530, Hameenlinna
Kuopio University Hospital
Pediatric Neurology, Puijonlaaksontie 2, P. O. Box 1777, Kuopio
Lapland Central Hospital
-, Ounasrinteentie 22, 96400, Rovaniemi

Country notifications

Trial-start, recruitment-start, end and early-termination notifications submitted per Member State

Country Trial startTrial end Recruitment startRecruitment end Early termination
Finland 2018-05-28 2018-09-15

Results and documents

Annex IV summary of results, Annex V layperson summary, and all documents registered in CTIS for this trial

Documents 13 files

Public protocol annexes, IB summaries, regulatory submissions and post-authorisation documents registered in CTIS.

TypeTitleVersion
Protocol (for publication) D1_ Protocol EU CT 2024-517488-22-00_version 1_6_clean version to be version 1_7 1.6
Protocol (for publication) Tutkimussuunnitelma _PREVIS 1.7
Recruitment arrangements (for publication) Liite 7 Selvitys suostumuksen saamiseksi noudatettavasta menettelysta 1
Subject information and informed consent form (for publication) L1_ICF_Finnish_versio 1_2_clean version to be version 1_3 1.2
Subject information and informed consent form (for publication) L1_SIS_english 1.5
Subject information and informed consent form (for publication) L1_SIS_english_version 1_4 1.4
Subject information and informed consent form (for publication) L1_SIS_Finnish_version 1_4_clean version to be version 1_5 1.4
Subject information and informed consent form (for publication) L1_SIS_Finnish_version 1_4_TSC patients_only redacted 1.4
Subject information and informed consent form (for publication) L1-ICF_English_versio 1_3_TC 1.3
Subject information and informed consent form (for publication) L1-ICF-English_version 1_2 1.2
Subject information and informed consent form (for publication) suostumuskaavake 1
Subject information and informed consent form (for publication) Tiedote tutkittavalle aivokuorivaurio PREV-IS 1.5
Synopsis of the protocol (for publication) DI_Protocol synopsis FIN 2024-517488-22-00 1

Application history

4 submissions — initial application plus substantial / non-substantial modifications

#TypeCodeSubmittedReference MSConclusionDecision date
1 INITIAL IN 2024-08-31 Finland Acceptable with conditions
2024-09-13
2024-09-13
2 SUBSTANTIAL MODIFICATION SM-3 2025-10-24 Finland Acceptable
2025-12-22
2026-01-02
3 NON SUBSTANTIAL MODIFICATION NSM-1 2026-03-12 Finland Acceptable
2025-12-22
2026-03-12
4 NON SUBSTANTIAL MODIFICATION NSM-2 2026-03-29 Finland Acceptable
2025-12-22
2026-03-29